Challenges of Surgical Management of Glaucoma in Aniridia: A Case Series
Abstract
Congenital Aniridia is a rare condition which is mainly associated with PAX6 gene mutations, though other genes such as FOXC1, PITX2 and CYP1B1 have also been implicated. 1 Glaucoma associated with Aniridia has been reported to be between 6% and 75% of patients 2 and though it usually occurs later in life, it can also be present at birth. Treatment of glaucoma is difficult and challenging 3due to the angle anomalies and the progressive angle changes that take place. Surgical intervention is the most commonly utilized mode of management to achieve good intraocular pressure (IOP) control.1
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