Orbital Alveolar Rhabdomyosarcoma Mimicking a Capillary Haemangioma: A Case Report
Abstract
Introduction: Rhabdomyosarcoma (RMS) is the most common malignant tumour of childhood[1]. Orbital RMS is a rare tumour with annual incidence of 4.3 cases per million children [1]. In approximately 10% of cases the primary site is the orbit [2]. Orbital RMS is usually seen in the first decade of life. Primary orbital RMS involves the orbit, eyelid, conjunctiva, and rarely, the uveal tract. The typical presentation is a rapid onset of unilateral proptosis, eyelid edema and ptosis. Capillary haemangioma (CH) is a common benign
orbital vascular tumour of childhood characterized by appearance at birth or shortly after birth, rapid increase in size for 6 to 12 months and then gradual involution over 5 to 7 years [3]. CH may cause proptosis or globe displacement [4].
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